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ELECTRONIC SUPPLEMENTARY MATERIAL

Online Resource 1.Survey tool.

Decision­making in decompressive craniectomy for malignant MCA syndrome

Thank you for agreeing to participate in this study.

Some cerebrovascular accidents (strokes) can lead to life­threatening brain swelling (malignant MCA syndrome). Decompressive craniectomy is a neurosurgical operation that involves removing a piece of skull to provide extra space for the brain to swell. This surgery is the only definitive option known to improve survival for life­threatening brain swelling following a stroke. However, the decision to operate on a patient can be complex, based on a combination of medical, social and ethical considerations.

Current evidence in patients under the age of 60 has demonstrated the following about decompressive craniectomy for malignant MCA syndrome:

1. The surgery improves survival at 1 year by 50% (78% vs 29%)

2. The surgery doubles the chance of being independent at 1 year (43% vs 21%)

3. The surgery increases the probability of survival in a condition requiring assistance by 15 times at 1 year (2% vs 31%)[Vahedi et al., Lancet Neurology, 2007].

There are currently no practice guidelines for when it is appropriate to offer a patient this procedure and the decision may depend on perception about the futility of care.

You will be presented with a series of vignettes involving decompressive craniectomy for malignant MCA syndrome. The first part of each vignette will describe the patient’s baseline characteristics – these are the only aspects that change from case to case and they are highlighted in red. The remainder of the vignette will be the same – all patients undergo the same course in hospital after their stroke. You will then be asked whether you agree or disagree with offering surgical decompression for each particular patient.

The variation in clinical practice in scenarios without clear "ethical" guidelines is a topic of growing interest. Your responses will help elucidate the importance of patient­specific factors in the decision­making process.

Thank you again for participating in this study.

Dr. Judy Illes, Professor of Neurology and Director, National Core of Neuroethics

Dr. Charles Haw, Professor of Neurosurgery

Dr. Danny Mendelsohn, PGY-1 Neurosurgery resident

1. What is your position?

Neurosurgery Staff

Neurosurgery Resident

Neurology Staff

Neurology Resident

Registered Nurse

Physiotherapist

Occupational Therapist

Speech Language Pathologist

Pharmacist

Social Worker

Dietician

Other (please specify)

2. How many years have you been in practice?

<5 years

5­9 years

10­14 years

>15 years

3. How many years have you been in training?

1

2

3

4

5

6

7

4. What is your gender?

Male

Female

Prefer not to disclose

5. What is your age?

<21

21­30

31­40

41­50

51­60

>60

You will be presented with a series of vignettes involving decompressive craniectomy for malignant MCA syndrome. The first part of each vignette will describe the patient’s baseline characteristics – these are the only aspects that change from case to case and they are highlighted in red. The remainder of the vignette will be the same – all patients undergo the same course in hospital after their stroke. You will then be asked whether you agree or disagree with offering surgical decompression for each particular patient.

6. A previously healthy and independent 55 year­old patient suffers a massive stroke on the right side of the brain. The patient is very weak in the left arm and leg.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the left arm and leg.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

7. A previously healthy and independent 55 year­old patient suffers a massive stroke on the left side of the brain. The patient is very weak in the right arm and leg and has severe language comprehension and speech production problems.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the right arm and leg and permanent language comprehension and speech production problems.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

8. A previously healthy and independent 70 year­old patient suffers a massive stroke on the right side of their brain. The patient is very weak in the left arm and leg.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the left arm and leg.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

9. A previously healthy and independent 70 year­old patient suffers a massive stroke on the left side of the brain. The patient is very weak in the right arm and leg and has severe language comprehension and speech production problems.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the right arm and leg and permanent language comprehension and speech production problems.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

10. A 70 year­old patient suffers a massive stroke on the right side of their brain. The patient is very weak in the left arm and leg. Prior to the stroke, the patient had dementia and lived in a nursing home. The patient could previously feed themselves but were unable to maintain personal hygiene without assistance and frequently forgot who their grandchildren were.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the left arm and leg.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

11. A previously healthy and independent 70 year­old patient suffers a massive stroke on the right side of the brain. The patient is very weak in the left arm and leg. The patient has no living relatives and has lost touch with all their friends.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the left arm and leg.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

12. A 70 year­old patient suffers a massive stroke on the right side of the brain. The patient is very weak in the left arm and leg. The patient's past medical history includes chronic kidney disease treated with dialysis and two previous heart attacks.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the left arm and leg.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

13. A previously healthy and independent 70 year­old patient suffers a massive stroke on the right side of the brain. The patient is very weak in the left arm and leg. Prior to the stroke, the patient was a three­time gold medalist in the Geriatric Olympics in the sport of tennis.

Three days later, the patient deteriorates neurologically and a CT scan reveals life­ threateningbrain­swelling. Surgical decompression can potentially save the patient’s life, but the patient is expected to have permanent weakness in the left arm and leg.

It is appropriate to offer the patient a decompressive craniectomy.

Strongly Disagree - Strongly Agree (9 point Likert scale)

Additional comments (optional):

14. This study has investigated the importance of the following factors in the decision to offer surgical decompression for malignant MCA syndrome.

Baseline functional status

Co­morbidities

Patient age

Permanent language impairment

Social supports

Are there any other factors that are important for decision­making in this case?

No

The following factor is important:

15. Please rate the importance of the following factors in the decision to offer surgical decompression for malignant MCA syndrome.

Permanent language impairment

Co­morbidities

Baseline functional status

Patient age

Social supports

Not important at all - Extremely important (9 point Likert scale)

16. Please rank the following factors in the decision to offer surgical decompression for malignant MCA syndrome (1 = most important, 6 = least important).

Permanent language impairment

Co­morbidities

Baseline functional status

Patient age

Social supports

[Factor entered from question 14]

Additional comments (optional):

17. The following questions pertain to the appropriate use of specifically decompressive craniectomy for malignant MCA syndrome.

It is appropriate to withhold this potentially life­saving operation based on:

Extent of neurologic deficits anticipated

Medical Co­morbidities

Baseline functional status

Patient age

Degree of social supports

Strongly Disagree - Strongly Agree (9 point Likert scale)

18. It is appropriate to withhold this potentially life­saving operation if the outcome is considered medically futile irrespective of the family’s wishes:

Strongly Disagree - Strongly Agree (9 point Likert scale)

19. In situations where it is unclear if it is appropriate to perform this operation, rate your agreement with each of the following steps:

Discuss the risks and benefits with the family/substitute decision­maker and allow that person to decide

Discuss the risks and benefits with the family/substitute decision­maker but do not offload the decision onto them

Discuss the risks and benefits with other clinicians

Discuss the risks and benefits with allied health professionals (eg. nurses, OT, PT) on the medical team

Discuss the risks and benefits with the clinical ethics team

When in doubt, perform the surgery

When in doubt, opt for conservative (non­operative) management

I don’t know

Strongly Disagree - Strongly Agree (9 point Likert scale)

Other (please specify)

20. In situations where it is unclear if it is appropriate to perform this potentially life­saving operation, rate the clinical ethics principles in order of importance for decision­making:

Autonomy ­ the right to refuse or choose treatment

Beneficence ­ act in the best interest of the patient

Non­maleficence ­ first, do no harm

Justice ­ fair distribution of health resources

Other (please specify)

21. Please add any comments here.

Thank you for participating in this study.

Online Resource 2.Demographic characteristics of study participants.

Neurosurgery Staff/Residents / Neurology Staff/Residents / Nurses & Allied Health / Total
Age / 21-30 / 6 (31.6%) / 13 (37.1%) / 12 (40.0%) / 31 (36.9%)
31-40 / 5 (26.3%) / 7 (20.0%) / 10 (33.3%) / 22 (26.2%)
41-50 / 5 26.3%) / 7 (20.0%) / 6 (20.0%) / 18 (21.4%)
51-60 / 0 / 5 (14.3%) / 2 (6.7%) / 7 (8.3%)
>60 / 3 (15.8%) / 3 (8.6%) / 0 / 6 (7.1%)
Gender / Male / 18 (94.7%) / 15 (44.1%) / 2 (6.7%) / 35 (42.2%)
Female / 0 / 16 (47.1%) / 28 (93.3%) / 44 (53.0%)
Prefer not to disclose / 1 (5.3%) / 3 (8.8%) / 0 / 4 (4.8%)
Training or
Years in Practice / Training / 7 (36.8%) / 15 (42.9%) / 0 / 22 (25.9%)
< 5 years / 3 (15.8%) / 5 (14.3%) / 9 (29.0%) / 17 (20.0%)
5-9 years / 3 (15.8%) / 1 (2.9%) / 10 (32.3%) / 14 (16.5%)
10-14 years / 1 (5.3%) / 4 (11.4%) / 4 (12.9%) / 9 (10.6%)
>15 years / 5 (26.3%) / 10 (28.6%) / 8 (25.8%) / 23 (27.1%)

Online Resource 3.Rating of agreement with options proposed for managing situations in which it is unclear whether or not the patient will benefit from hemicraniectomy.

Proposed Option / Average 9-point Likert Rating / Percentage Agreement
Discuss the risks and benefits with other clinicians / 7.43 / 82.6
Discuss the risks and benefits with the substitute decision-maker and allow that person to decide / 6.61 / 73.4
Discuss the risks and benefits with the clinical ethics team / 6.27 / 69.7
Discuss the risks and benefits with the substitute decision-maker but do not offload the decision onto them / 6.12 / 68.0
Discuss the risks and benefits with allied health professionals (eg. nurses, OT, PT) on the medical team / 5.64 / 62.7
When in doubt, opt for conservative (non-operative) management / 4.81 / 53.4
When in doubt, perform the surgery / 4.33 / 48.1
I don’t know / 4.10 / 45.6