Biochemistry Objectives 50
1.Androgen biosynthesis:
- Testicular pathway: cholesterol is converted into pregnenolone via P-450scc pregnenolone is converted to progesterone via 3OH-SD, 5,4 isomerase progesterone is converted to 17--progesterone by 17--hydroxylase 17--hydroxylase is converted to androstenedione by C17-20 lyase androstenedione is converted to testosterone via 17-hydroxysteroid dehydrogenase testosterone is converted to dihydrotestosterone via 5reductase-2
- Mechanism of stimulation: the process is stimulated via LH stimulation of P-450scc, the enzyme that catalyzes the conversion of cholesterol to pregnenolone
2.Estrogen biosynthesis:
- General pathway: follows the same pathway as testosterone, with the following caveats: androstenedione can form estrone (E1) via aromatase (19-hydroxylase) in adipose cells, testosterone can form 17-estradiol (E2) from aromatase in granulose cells, and DHEA can be 16-hydroxylated and modified to form estriol (E3). Note that E1, E2, and E3 can interconvert; E1 is oxidized E2, and E2 can be 16-hydroxylated to form E3.
- Location of LH stimulation (P-450scc): LH stimulation occurs in the thecal cells (initial formation of androgen)
- Location of FSH stimulation (aromatase): FSH stimulation occurs in the granulosa cells (formation of E2)
- Location of androstenedione aromatization: androstenedione aromatization occurs in the fetal liver/placenta (formation of E3)
3.Dihydrotestosterone:
- Enzyme that catalyzes its formation: 5--reductase
- Sites of production: produced mainly in peripheral tissues, though the testes secrete 50-100 μg per day
- Target tissues: targets the external genitalia (also prostate and genital skin) to induce male proliferation of external genitalia
- Role in benign prostatic hyperplasia: DHT induces the proliferation of the prostate, and with high levels of DHT in older men, the prostate will grow rapidly causing benign prostatic hyperplasia
- Role of 5--reductase-2 inhibitors in BPH treatment: since DHT is the main cause of benigh prostatic hyperplasia, treatment with 5--reductase-2 inhibitors will cause a lowered production of DHT and less stimulation of the prostate
4.Phenotypes, biochemistry, and pathophysiology of:
a.17-hydroxylase deficiency: inability to produce any of the sex hormones, and a hypogonadism due to decreased external genital differentiation stimulation
b.5--reductase-2 deficiency: inability to produce DHT, and a female external genital phenotype at birth that progresses to male hypogonadism as testosterone exerts its weaker effect to produce male external genitalia
c.Androgen receptor mutation: in XY patients, testicular formation occurs due to SRY region of the Y chromosome; however, since the body is insensitive to both testosterone and DHT, the patient makes no Wolffian structures, and the external genitalia is feminine.
5.Osteoporosis:
- Estrogen/androgen protection: estrogen acts as an inhibitor of both PTH and peripheral blood monocytes. Therefore, due to peripheral blood monocyte inhibition, estrogen causes a decrease in IL-1 and M-CSF, blocking osteoclast differentiation and protecting bone from resorption.
- Phytoestrogen nutritional value: phytoestrogens are controversial estrogen-like compounds found in foods that potentially have a beneficial effect due to their estrogen-like activity.